Ameloblastic fibro-odontoma has been defined as a lesion similar to ameloblastic fibroma by WHO, as it shows inductive changes which forms enamel and dentin. Ameloblastic fibro-odontoma is a very rare mixed dentition tumor in children, and the symptom shows indolent edema in maxillary and mandibular molar area. The prevalence is two times higher in male than in female, and two times higher in maxilla than in mandible. Radiologically, it shows clear border and characteristics of both fibroma and odontoma histologically. This review reports a case that a 4-year old female visited in dental clinic of this school for edema as chief complaint in Feb, 2012. Emergency surgical curettage was performed right after initial diagnosis as odontoma, then confirmed diagnosis as Ameloblastic fibro- odontoma after biopsy. Currently, after 6 month, no sign of recurrence can be seen. Ameloblastic fibro-odontoma is very rare mixed dentition tumor. Moreover, as it is the case of female maxilla, this case is worth of publishing. Furthermore, accurate diagnosis of Ameloblastic fibro-odontoma is difficult. This review is published for accurate diagnosis through differential diagnosis of several important mixed dentition tumors.

Ⅰ. Introduction
 Ⅱ. Case report
 Ⅲ. Discussion and Literature review
 Ⅳ. References

• 박원홍(Dental Science Research Institute and Medical Research Center for Biomineralization Disorders, School of Dentistry, Chonnam National University) | Won Hong Park
• 임원봉(Dental Science Research Institute and Medical Research Center for Biomineralization Disorders, School of Dentistry, Chonnam National University) | Won Bong Lim
• 김지선(Dental Science Research Institute and Medical Research Center for Biomineralization Disorders, School of Dentistry, Chonnam National University) | Ji Sun Kim
• 김상우(Dental Science Research Institute and Medical Research Center for Biomineralization Disorders, School of Dentistry, Chonnam National University) | Sang Woo Kim
• Zheng Hui(Dental Science Research Institute and Medical Research Center for Biomineralization Disorders, School of Dentistry, Chonnam National University)
• Kou Ni(Dental Science Research Institute and Medical Research Center for Biomineralization Disorders, School of Dentistry, Chonnam National University)
• 전상미(Dental Science Research Institute and Medical Research Center for Biomineralization Disorders, School of Dentistry, Chonnam National University) | Sang Mi Jeon
• 박지일(Department of Dental Hygiene, Gwangju Health University) | Ji Il Park
• 최홍란(Dental Science Research Institute and Medical Research Center for Biomineralization Disorders, School of Dentistry, Chonnam National University) | Hong Ran Choi
• 김옥준(Dental Science Research Institute and Medical Research Center for Biomineralization Disorders, School of Dentistry, Chonnam National University) | Ok Joon Kim correspondence