A 48-year-old woman visited the oral and maxillofacial surgery department complaining of swelling under the left mandible. The patient said that the size of the small lump had not changed much since it was first discovered, but it seemed to have grown slightly recently after 5 years. She visited another hospital 1 week ago and had a CT scan, but no specific findings were found. A firm and mobile mass was palpated in the submandibular gland area during clinical examination. Ultrasound imaging and contrast-enhanced CT were performed, and the patient was diagnosed with pleomorphic adenoma. Submandibular gland resection was performed, and the mass was confirmed as pleomorphic adenoma by histopathological examination. There has been no recurrence to date, 8 years later. In this study, we will examine the diagnostic process of a rare submandibular gland pleomorphic adenoma and review the literature.