KOREASCHOLAR

Galactosemia is a rare, hereditary metabolic disorder caused by the accumulation of galactose and its metabolites in the body due to a lack of enzymes that convert galactose to glucose. This study aimed to investigate the dietary behaviors and nutritional statuses of patients with galactosemia and to provide basic information on the development of nutrition education programs to improve quality of dietary life. A survey was conducted on 13 parents of (<11 years of age) children with galactosemia and 26 parents of (<11 years of age) children without galactosemia. Mean body mass index was greater for school-age children with galactosemia (18.77 kg/m2) than for corresponding normal children (16.55 kg/m2). Underweight and obesity rates of children with galactosemia were greater than those of children without galactosemia. In addition, children with galactosemia had a higher food neophobia rate and thus consumed less food. Normal children exhibited a greater range of food preferences than those with galactosemia, especially for milk and dairy products (p= .001) and fats and sweets (p= .04). Reliable food databases and appropriate dietary recommendations are required to ensure the proper growth of children with galactosemia.

Abstract
I. 서 론
II. 연구 내용 및 방법
    1. 연구대상 및 기간
    2. 측정 도구
    3. 통계분석
III. 결과 및 고찰
    1. 조사대상자인 부모의 일반적 특성
    2. 질환 유무에 따른 영양상태 비교
    3. 부모가 인지하는 자녀의 푸드네오포비아, 건강과 관련된 삶의 질
    4. 식품군별 기호도 및 교육요구
    5. 식이섭취 현황
    6. 영양지수, FNS, 건강과 관련된 삶의 질 변수 간의 상관관계
IV. 요약 및 결론
감사의 글
Conflict of Interest
References

• 서혜지(이화여자대학교 식품영양학과) | Hye Ji Seo (Department of Nutritional Science and Food Management, Ewha Womans University)
• 정예승(이화여자대학교 식품영양학과) | Yeseung Jeong (Department of Nutritional Science and Food Management, Ewha Womans University)
• 김유리(이화여자대학교 식품영양학과) | Yuri Kim (Department of Nutritional Science and Food Management, Ewha Womans University)
• 오지은(이화여자대학교 신산업융합대학) | Jieun Oh (College of Science and Industry Convergence, Ewha Womans University) Corresponding author