Urachal cancer is extremely rare and accounts for fewer than 1% of malignant neoplasms of the bladder. Urachal remnants persist from the bladder dome to umbilicus after birth, and urachal carcinoma may arise from any of these segments. The standard treatment for urachal cancer is primarily wide excision with extended partial cystectomy of the urachal mass, urachal tract and umbilicus, and pelvic lymph node dissection. Nevertheless, prognosis is generally poor because early diagnosis is difficult and local invasions, distant metastasis, and recurrence frequently develop. The authors present a patient with recurred urachal adenocarcinoma, who was treated by partial cystectomy with lymph node dissection. One year after subsequent concurrent chemoradiotherapy, she achieved complete remission. A brief review of the literature on urachal adenocarcinoma is provided.