서론 : 본 연구의 목적은 선천성 척수성 근 위축증 환자에게 고급보조공학을 적용한 사례연구를 통하여 고급보조 공학 적용의 확대와 관심을 높이는데 있다. 본론 : 대학병원에서 재활치료를 받고 있는 선천성 척수성 근위축증 2형(SMA type II)인 중증장애인에게 고급보조공학 기기인 동공인식보조기기(TM 2)를 이용한 사례를 보고하였다. 기본적인 의사소통뿐 아니라 보호자의 도움을 받지 못하면 스스로 전혀 할 수 없었던 활동영역이 보조공학기기의 적용으로 확대되면서, 전반적인 의사소통 및 일상생활활동의 자신감이 향상되었다. 결론 : 척수성 근 위축증 환자는 모든 일상생활과 기타활동에 전적으로 보호자에게 의존해야 하지만, 고급보조공학의 사용으로 여러 가지 활동을 스스로 할 수 있었다. 이러한 결과로 고급보조공학의 적절한 적용은 다른 중증장애인에게도 삶의 질을 높일 수 있는 큰 역할을 할 수 있을 것으로 기대된다.

In children with cerebral palsy, bone density is decreased by disturbance of bone remodelling due to lack of normal weight bearing and muscle contraction through physical activity. Loss of bone density cause fracture, delays treatment with immobilization, and leads to functional limitation. The purpose of this study was to investigate bone mineral density of lumbar spine in children with spastic quadriplegia and diplegia. Six spastic quadriplegia and 14 spastic diplegia were evaluated in this study. QDR 4500 X-ray densitometer was used to measure bone density at lumbar spine (L1~L4). Children with cerebral palsy showed lower bone density than that of normal children. Bone density in children with spastic quadriplegia and diplegia was , , respectively. However, there was no significant differences in bone density between children with spastic quadriplegia and diplegia. There was no significant difference in bone density relation to motor development level, height, and weight. Further study is needed to find the appropriate interventions for preventing loss of bone density in children with cerebral palsy.

The purpose of this study was to investigate the relation between components of population, maternal health, need for health care, maternal lifestyle and environment from a conceptual model for cerebral palsy, and the occurrence of cerebral palsy with spastic quadriplegic. This study was a case-control design. The subjects consisted of 53 children with quadriplegic cerebral palsy as a case who were receiving treatment after a diagnosis for cerebral palsy at 3 university hospitals and 3 rehabilitation facilities, and 186 children as a control who were visiting well baby clinics and pediatric departments after screening at the same hospitals in Seoul. The data were collected by a structured questionnaire survey from October, 1998 to February, 1999. The odds ratios of risk factor was produced by χ2 and simple logistic analysiss. The unconditional logistic analysis was done by modeling the data, after adjusting for gestational age. Statistically associated with an increase the risks for spastic quadriplegia were asphyxia(OR=221.89, 95% CI 15.8-999.0) and maternal history of admission during the pregnancy (OR=10.55, 95% CI 2.2-50.4). The result suggested that the improvement of obstetric and neonatal care is necessary to prevent cerebral palsy with spastic quadriplegia.